Here is the translated text: # What Is Chronic Thromboembolic Pulmonary Hypertension? Chronic thromboembolic pulmonary hypertension (CTEPH) is a type of pulmonary hypertension that affects people in different ways. ## Symptoms The symptoms of CTEPH can vary from person to person, but may include:

• Shortness of breath, especially during physical activity.
• Swollen legs due to fluid retention (edema).

## Diagnosis and Tests Your care may start with tests to check for signs of CTEPH. These include:

• Lung ventilation-perfusion scan (V/Q scan).
• Pulmonary angiogram, which shows whether there are blood clots or narrow blood vessels.
• Pulmonary function tests.
• Transthoracic echocardiogram (TTE).

Additional studies are typically necessary. They help confirm a chronic thromboembolic pulmonary hypertension diagnosis and its severity. You may need:

• Right heart catheterization.
• CT pulmonary or digital subtraction angiography. These tests use advanced imaging techniques to check your pulmonary arteries.
• MRI.
• Exercise stress test.

## Management and Treatment A procedure is typically necessary. There are two options:

1. Pulmonary endarterectomy: This open surgical procedure removes blood clots from your lung arteries.
2. Pulmonary balloon angioplasty: This procedure uses tiny balloons at the tip of long tubes (catheters). They push aside scar tissue to open up narrowed arteries.

## Additional Treatment Options Riociguat tablets, a pulmonary hypertension medication, can bring some symptom relief. This drug is for people who can't have a procedure. It’s also for patients whose pulmonary hypertension continues after surgery. ## Prevention CTEPH is a complication of many health conditions, some of which are out of your control. You can lower your risk by taking good care of your lungs. This includes avoiding tobacco or quitting smoking. ## Outlook / Prognosis Pulmonary endarterectomy and pulmonary balloon angioplasty can potentially cure CTEPH. People who have one of these procedures typically have an excellent prognosis. Despite this positive outlook, many patients struggle with anxiety and depression. If you experience these issues, let your healthcare provider know. They can address your concerns and recommend therapies to help you feel better. ## Living With You'll be on blood thinners for the rest of your life. If you take warfarin, you might have to avoid certain foods. These include foods high in vitamin K, like soy and broccoli. Light exercise, like walking, helps many people gain strength and feel their best. Your healthcare provider may recommend a medically supervised exercise program(pulmonary rehabilitation). Key Takeaways Chronic thromboembolic hypertension is a form of pulmonary hypertension. It's a rare condition that causes high blood pressure in the small vessels of the lungs. CTEPH is potentially curable if you undergo a procedure. Many people who receive treatment for this condition have an excellent prognosis.